National Organization for Rare Disorders, Inc.Cirrhosis, Primary BiliaryImportant
It is possible that the main title of the report Cirrhosis, Primary Biliary
is not the name you expected. Please check the synonyms listing to find
the alternate name(s) and disorder subdivision(s) covered by this report.
SynonymsDisorder SubdivisionsGeneral DiscussionPrimary biliary cirrhosis (PBC) is a chronic progressive liver disorder that primarily affects females and typically becomes apparent during middle age. Obstruction of the small bile ducts is accompanied by yellow discoloration of the skin (jaundice). Excessive amounts of copper accumulate in the liver, and fibrous or granular hardening (induration) of the soft liver tissue develops. The course of primary biliary cirrhosis is divided into four progressive stages. Although the exact cause of primary biliary cirrhosis is unknown, possible immunological, autoimmune, genetic, and/or environmental factors are under investigation as potential causes of the disorder. . ResourcesAmerican Autoimmune Related Diseases Association, Inc. 22100 Gratiot Avenue Eastpointe, MI 48021-2227 Tel: (586)776-3900 Fax: (586)776-3903 Tel: (800)598-4668 Email: aarda@aarda.org Internet: http://www.aarda.org/
American Liver Foundation 75 Maiden Lane Suite 603 New York, NY 10038 USA Tel: 2126681000 Fax: 2124838179 Tel: 8004654837 Email: info@liverfoundation.org Internet: http://www.liverfoundation.org
NIH/National Digestive Diseases Information Clearinghouse 2 Information Way Bethesda, MD 20892-3570 Tel: (301)654-3810 Fax: (301)907-8906 Tel: (800)891-5389 Email: nddic@info.niddk.nih.gov Internet: http://www.niddk.nih.gov
Primary Biliary Cirrhosis Support Group 1430 Garden Road Pearland, TX 77581 USA Tel: 2814129161 Fax: 2814129161 Email: PBCers@aol.com Internet: http://www.pbcers.org
Autoimmune Information Network, Inc PO Box 4121 Brick, NJ 08723 Tel: (732)262-0450 Fax: (732)262-0450 Email: autoimmunehelp@aol.com Internet: http://www.aininc.org
European Society for Immunodeficiencies (ESID) c/o Dr. Esther de Vries Jeroen Bosch Hospital Dept. Paediatrics P.O. Box 90153 Hertogenbosch, 5200 ME's Netherlands Tel: +31 73-6992965 Fax: +31 73-6992948 Email: info@esid.org Internet: http://www.esid.org
AutoImmunity Community
Tel: (919)-55-2-9057 Email: bandrews@autoimmunitycommunity.org Internet: http://autoimmunitycommunity.org
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Last Updated: 8/7/2007
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National Organization for Rare Disorders, Inc.
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